Pediatric Synovial Sarcoma in the Retropharyngeal Space: A Rare and Unusual Presentation

نویسندگان

  • Sanjay Vaid
  • Neelam Vaid
  • Sanjay Desai
  • Varada Vaze
چکیده

Synovial sarcomas in the head and neck are extremely rare tumors, especially in the pediatric population. 3-5% of synovial sarcomas occur in the head and neck region displaying varied imaging and histopathological features resulting in frequent misdiagnosis. These tumors have a poor prognosis; hence early diagnosis and accurate classification based on imaging, histopathology, and immunohistochemistry are critical for prompt treatment. To the best of our knowledge, imaging findings of pediatric retropharyngeal lipomatous synovial sarcoma have not been reported to date in English medical literature. We report, for the first time, a rare case of retropharyngeal lipomatous synovial sarcoma in a ten-year-old child and discuss the case-specific imaging findings in our patient using magnetic resonance imaging and computed tomography.

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عنوان ژورنال:

دوره 2015  شماره 

صفحات  -

تاریخ انتشار 2015